Meyer dysplasia: a diagnosis to consider.

نویسندگان

  • Ana Teresa Maria
  • Raquel Firme
  • Pedro Magro
  • Sílvia Jorge
چکیده

To cite: Maria AT, Firme R, Magro P, et al. BMJ Case Rep Published online: [please include Day Month Year] doi:10.1136/bcr-2015214282 DESCRIPTION A 2-year-old boy with unremarkable medical history presented to the emergency room due to sudden onset of left hip pain and limping gait, without fever or trauma. On observation, he had no signs of inflammation and no limitation of joint mobilisation. Hip radiography revealed widening of the medial joint space and a smaller, irregular, ossification nucleus of the proximal left femur, with no condensation and no other epiphysial changes (figure 1). Laboratory data showed no elevated inflammatory parameters. The patient was submitted to hip ultrasonography, which excluded effusion; and CT scan, which confirmed the X-ray findings. The diagnosis of Meyer dysplasia (MD) was then suggested and symptoms resolved within a few days with minimal analgaesia. At the age of 4, he remains asymptomatic with progressive radiological improvement at orthopaedic follow-up. MD is a rare hip developmental disorder, characterised by delay and irregularity of ossification of the proximal epiphysial nucleus of the femur. 2 The differential diagnosis consists mainly of Perthes disease (PD). Recent series suggest that up to 5% of patients initially diagnosed with PD have MD. In MD, there are multiple independent ossification foci, which gradually coalesce to form a single nucleus. Unlike PD, there are no aspects of epiphysial condensation, fragmentation, subchondral fractures or collapse. Symptoms, when present, are mild and transient. The diagnosis can be achieved by plain radiography, not requiring additional investigations. Evolution is favourable, with the epiphysis reaching normal shape and size. 3 Treatment is not necessary and prognosis is good. 3 Clinical and radiographic surveillance is recommended to document resolution. 3

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عنوان ژورنال:
  • BMJ case reports

دوره 2016  شماره 

صفحات  -

تاریخ انتشار 2016